XÜLASƏ
Zülal itkisi ilə gedən enteropatiya (ZİE) – bağırsaq xəstəliklərində rast gəlinən nadir və mürəkkəb ağırlaşmalardan biri hesab edilir. Bu patologiyanın əsas əlaməti hipoproteinemik ödemlərin əmələ qəlməsidir. Xəstəliyin diaqnostikası nəcisdə α1- antitripsinin təyini vasitəsilə bağırsaq boşluğuna zülal itkisinin verifikasiyasına əsaslanır. Bağırsağın zədələnmiş seqmentini şüa və endoskopik diaqnostika metodları ilə müəyyən edirlər. Müalicənin əsasını ortazəncirli triqliseridlərlə zəngin yağsız pəhriz təşkil edir. Medikamentoz müalicəyə tabe olmayan ağır hipoproteinemiyalar zamanı seçim cərrahi müalicədir- zədələnmiş seqmentin rezeksiyasıdır.
Açar sözlər: zülal itkisi ilə qedən enteropatiya, alfa-1-antitripsin, hipoalbuminemiya

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ƏDƏBİYYAT

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