РЕЗЮМЕ
Энтеропатия с потерей белка (ЭПБ) считается одним из редких и сложных осложнений кишечных заболеваний. Основным признаком данной патологии является формирование гипопротеинемических отеков. Диагностика заболевания основана на верификации потери белка путем определения α1-антитрипсина в кале. Поврежденный сегмент кишки выявляют при помощи рентгенологических и эндоскопических методов диагностики. Основой лечения является диета с низким содержанием жиров, богатая средне- цепочечными триглицеридами. В случаях тяжелых гипопротеинемий, не поддающихся медикаментозному лечению, выбором является оперативное лечение – резекция поврежденного сегмента.
Keywords: энтеропатия с потерей белка, альфа-1-антитрипсин, гипоальбуминемия

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ЛИТЕРАТУРА

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